Mohd Vaseem J¹, Satish Chandra K² , Prasad C N³, Ramulu M⁴

¹Postgraduate Student, ²Professor & HOD, ³Professor, ⁴ Assitant Professor, Department of Respiratory Medicine, Prathima Institute of Medical Sciences, Karimnagar, Telangana, India.

Address for correspondence: Dr Mohd Vaseem, Postgraduate Student, Department of Respiratory Medicine, Prathima Institute of Medical Sciences, Karimnagar, Telangana, India.

Email: mohdvaseemj@gmail.com

Pulmonary Alveolar Microlithiasis (PAM) is a rare, slowly progressive lung disease, characterised by widespread intra-alveolar accumulation of minute calculi called microliths. It is caused by mutation in SCL34A2 gene encoding sodium phosphate cotransporter in alveolar type II cells. Herein, we report a case of PAM, diagnosed incidentally showing “Sandstorm” appearance on chest X ray. Diagnosis was confirmed based on characteristic features of PAM on HRCT Chest scan and striking clinico-radiological dissociation.

Keywords : Microlithiasis, Pulmonary, alveolar, Sandstorm, SCL34A2 gene, microliths.