Volume: 7 Issue: 2
Year: 2019, Page: 82-84,
Paragangliomas arise from para ganglion cells. These are slow growing tumors (< 2 cm in 5 years) and are histologically benign (< 10% associated with lymphnode involvement or distant spread). Most contain secretory granules on electron microscopy (mostly epinephrine & norepinephrine, and these tumors may occasionally secrete these catecholamines with risk of life-threatening hypertension and/ or cardiac arrhythmias). Carotid bifurcation most common site. Spinal paragangliomas are very rare neuroendocrine tumors often presenting with low back pain and radicular symptoms. Radiographically spinal paragangliomas mimic more commonly described tumors, such as ependymomas, schwannomas, meningiomas, and even hemangiomas, but a "salt and pepper" appearance related to a serpiginous vascular structure is instructive. Indeed, the rarity of this tumor makes the diagnosis rather challenging radiographically. We report a case of 55yrs old female patient with clinical presentation like lumbar canal stenosis on evalution found intra dural spinal canal tumor at L3and L4 vertebra,suspected to be schwanomma radiologically. After excision of the specimen and sent for histopathological examination suggestive of ependymoma. After immunohistochemistry study of tumor found to be paraganglioma.
Keywords: Paraganglioma, Spinal Tumour, Intradural Tumour
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Sanjeev Kumar A,Anandam G,Vikas Ch,subramanyam ,Laxmi. Spinal paraganglioma presenting as a lumbar canal stenosis – a rare case report. Perspectives in Medical Research 2019; 7(2):82-84.